一、概述
风湿病:影响骨、关节及其周围软组织炎症
目录
二、风湿病特点
1. 自身免疫病
2. 全身多个系统疾病
3. 临床表现差异大
4. 用免疫抑制剂(早发现/早诊断/早治疗)
5. 结缔软组织/血管炎/韧带炎
三、分类
1、弥漫性结缔组织病,CTD
①干→干燥综合征
②湿→类风湿关节炎
③硬→系统性硬化(硬化病)
④朗→系统性红斑狼疮
⑤鸡→多肌炎
2、脊柱关节病
强直性脊柱炎、反应性关节炎(Reiter综合征)、银屑性关节病......
3、退行性关节病
骨关节炎(关节软骨退变)
4、晶体相关病
痛风
5、感染相关病
风湿热(β-溶血链)
6、其他
四、表现
1.类风湿
- 发病缓
- 双手、对称、多发、小关节病变
- 近段指间关节、掌指关节、腕关节
- 休息后加重
2.骨关节炎
- 发病缓
- 负重大关节
- 髋关节、膝关节、远端指间关节
- 活动后加重
3.强直性脊柱炎
- 起病缓
- 侵蚀中轴骨
- 骶髂关节→自下而上发展→脊柱
- 活动后减轻
总结:类风湿→上肢、痛风→下肢
4.痛风
- 起病急
- 夜间&凌晨发病、剧烈疼痛
- 第一跖趾关节
5.SLE
- 起病缓
- 多个系统病变→狼疮肾炎→尿蛋白(+)
- 多个关节疼痛(双手小关节)
五、特殊表现
1.SLE
面部蝶形红斑;盘状红斑;尿Pr(+)
2.干燥综合征
口干,眼干,牙齿破坏
3.皮肌炎
肌无力+Gottron征(口诀:出G蛋)
4.多发性硬化
皮肤硬肿+雷诺缺血
5.贝赫切特征
口腔溃疡+会阴溃疡
6.血管炎
鞍鼻
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很不错,学习一下
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